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11Mental Retardation and Isoleucine Metabolism, Branched Chain Amino Acids in Clinical Nutrition Propionyl-CoA carboxylase deficiency with overflow of metabolites of isoleucine catabolism at all levels, European Journal of Pediatrics Barth Syndrome: Connecting Cardiolipin to Cardiomyopathy, Lipids Metabolic Profile of Biological Constituents: (1) The Effects of Sodium Dipropylacetate on Human Urinary Acids, Recent Developments in Mass Spectrometry in Biochemistry and Medicine Metabolism of Amino Acids and Organic Acids, The Year in Metabolism 1975?1976 Branched Chain Amino Acid Oxidation Disorders, Branched Chain Amino Acids in Clinical Nutrition Profound neurological illness, relieved by protein restriction, in a baby with a transient disturbance in the metabolism of ingested isoleucine, European Journal of Pediatrics Excessive excretion of ??-alanine and of 3-hydroxypropionic,R- andS-3-aminoisobutyric,R- andS-3-hydroxyisobutyric andS-2-(hydroxymethyl)butyric acids probably due to a defect in the metabolism of the corresponding malonic semialdehydes, Journal of Inherited Metabolic Disease Self-assembly of segmented polyurethane and poly(4-vinylpyridine) in solution, Polymer Bulletin Optimization conditions for the separation of rare earth elements, americium, curium and cesium with HPLC technique, Journal of Radioanalytical and Nuclear Chemistry